LymphedemaV1, Main, Exploration, bibRecord, 012A39

Purpura-associated congenital lymphedema.

Identifieur interne : 012A39 ( Main/Exploration ); précédent : 012A38; suivant : 012A40

Purpura-associated congenital lymphedema.

Auteurs : Samantha Berti [Italie] ; Alessandro Pieri ; Torello Lotti ; Alberto Duranti ; John Panelos ; Maurizio De Martino ; Silvia Moretti

Source :

European journal of dermatology : EJD [ 1167-1122 ]

RBID : pubmed:19620038

Descripteurs français

KwdFr :
- Bas de contention, Cuisse (anatomopathologie), Dermatoses papulosquameuses (), Dermatoses papulosquameuses (diagnostic), Diagnostic différentiel, Enfant, Femelle, Genou (anatomopathologie), Glucocorticoïdes (usage thérapeutique), Humains, Lymphoedème (), Lymphoedème (diagnostic), Orteils (malformations), Purpura (), Purpura (diagnostic), Résultat thérapeutique, Syndactylie (), Syndrome, Veine saphène (), Veine saphène (anatomopathologie).
MESH :
- anatomopathologie : Cuisse, Genou, Veine saphène.
- diagnostic : Dermatoses papulosquameuses, Lymphoedème, Purpura.
- malformations : Orteils.
- usage thérapeutique : Glucocorticoïdes.
- Bas de contention, Dermatoses papulosquameuses, Diagnostic différentiel, Enfant, Femelle, Humains, Lymphoedème, Purpura, Résultat thérapeutique, Syndactylie, Syndrome, Veine saphène.

English descriptors

KwdEn :
- Child, Diagnosis, Differential, Female, Glucocorticoids (therapeutic use), Humans, Knee (pathology), Lymphedema (complications), Lymphedema (congenital), Lymphedema (diagnosis), Lymphedema (therapy), Purpura (complications), Purpura (diagnosis), Purpura (therapy), Saphenous Vein (pathology), Saphenous Vein (surgery), Skin Diseases, Papulosquamous (complications), Skin Diseases, Papulosquamous (diagnosis), Skin Diseases, Papulosquamous (therapy), Stockings, Compression, Syndactyly (complications), Syndrome, Thigh (pathology), Toes (abnormalities), Treatment Outcome.
MESH :
- chemical , therapeutic use : Glucocorticoids.
- abnormalities : Toes.
- complications : Lymphedema, Purpura, Skin Diseases, Papulosquamous, Syndactyly.
- congenital : Lymphedema.
- diagnosis : Lymphedema, Purpura, Skin Diseases, Papulosquamous.
- pathology : Knee, Saphenous Vein, Thigh.
- surgery : Saphenous Vein.
- therapy : Lymphedema, Purpura, Skin Diseases, Papulosquamous.
- Child, Diagnosis, Differential, Female, Humans, Stockings, Compression, Syndrome, Treatment Outcome.

Abstract

An 8-year-old girl referred to our Department for a two-month worsening of congenital primary lymphedema of the lower limb and for the appearance of several purpuric lesions on the right thigh and knee. We diagnosed a lichenoid pigmented purpura of Gougerot and Blum in a patient with Milroy disease, complicated by an insufficiency of anterior saphena. We treated the patient with topical steroids and compression stockings, until surgical intervention of phlebectomy. We report this case for the rarity of the disease, for the even more rare association with lichenoid pigmented purpura and for cutaneous immunopathological findings.

DOI: 10.1684/ejd.2009.0758
PubMed: 19620038

Affiliations:

Italie

Le document en format XML

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<author><name sortKey="Berti, Samantha" sort="Berti, Samantha" uniqKey="Berti S" first="Samantha" last="Berti">Samantha Berti</name>
<affiliation wicri:level="1"><nlm:affiliation>Department of Pediatric Medicine, Anna Meyer Children's Hospital, Viale Pieraccini, 24, 50132 Florence, Italy. bertis@masternet.it</nlm:affiliation>
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Department of Pediatric Medicine, Anna Meyer Children's Hospital, Viale Pieraccini, 24, 50132 Florence</wicri:regionArea>
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<author><name sortKey="Pieri, Alessandro" sort="Pieri, Alessandro" uniqKey="Pieri A" first="Alessandro" last="Pieri">Alessandro Pieri</name>
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<author><name sortKey="Lotti, Torello" sort="Lotti, Torello" uniqKey="Lotti T" first="Torello" last="Lotti">Torello Lotti</name>
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<author><name sortKey="Duranti, Alberto" sort="Duranti, Alberto" uniqKey="Duranti A" first="Alberto" last="Duranti">Alberto Duranti</name>
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<author><name sortKey="Panelos, John" sort="Panelos, John" uniqKey="Panelos J" first="John" last="Panelos">John Panelos</name>
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<author><name sortKey="Panelos, John" sort="Panelos, John" uniqKey="Panelos J" first="John" last="Panelos">John Panelos</name>
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<author><name sortKey="De Martino, Maurizio" sort="De Martino, Maurizio" uniqKey="De Martino M" first="Maurizio" last="De Martino">Maurizio De Martino</name>
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<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Child</term>
<term>Diagnosis, Differential</term>
<term>Female</term>
<term>Glucocorticoids (therapeutic use)</term>
<term>Humans</term>
<term>Knee (pathology)</term>
<term>Lymphedema (complications)</term>
<term>Lymphedema (congenital)</term>
<term>Lymphedema (diagnosis)</term>
<term>Lymphedema (therapy)</term>
<term>Purpura (complications)</term>
<term>Purpura (diagnosis)</term>
<term>Purpura (therapy)</term>
<term>Saphenous Vein (pathology)</term>
<term>Saphenous Vein (surgery)</term>
<term>Skin Diseases, Papulosquamous (complications)</term>
<term>Skin Diseases, Papulosquamous (diagnosis)</term>
<term>Skin Diseases, Papulosquamous (therapy)</term>
<term>Stockings, Compression</term>
<term>Syndactyly (complications)</term>
<term>Syndrome</term>
<term>Thigh (pathology)</term>
<term>Toes (abnormalities)</term>
<term>Treatment Outcome</term>
</keywords>
<keywords scheme="KwdFr" xml:lang="fr"><term>Bas de contention</term>
<term>Cuisse (anatomopathologie)</term>
<term>Dermatoses papulosquameuses ()</term>
<term>Dermatoses papulosquameuses (diagnostic)</term>
<term>Diagnostic différentiel</term>
<term>Enfant</term>
<term>Femelle</term>
<term>Genou (anatomopathologie)</term>
<term>Glucocorticoïdes (usage thérapeutique)</term>
<term>Humains</term>
<term>Lymphoedème ()</term>
<term>Lymphoedème (diagnostic)</term>
<term>Orteils (malformations)</term>
<term>Purpura ()</term>
<term>Purpura (diagnostic)</term>
<term>Résultat thérapeutique</term>
<term>Syndactylie ()</term>
<term>Syndrome</term>
<term>Veine saphène ()</term>
<term>Veine saphène (anatomopathologie)</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="therapeutic use" xml:lang="en"><term>Glucocorticoids</term>
</keywords>
<keywords scheme="MESH" qualifier="abnormalities" xml:lang="en"><term>Toes</term>
</keywords>
<keywords scheme="MESH" qualifier="anatomopathologie" xml:lang="fr"><term>Cuisse</term>
<term>Genou</term>
<term>Veine saphène</term>
</keywords>
<keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Lymphedema</term>
<term>Purpura</term>
<term>Skin Diseases, Papulosquamous</term>
<term>Syndactyly</term>
</keywords>
<keywords scheme="MESH" qualifier="congenital" xml:lang="en"><term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en"><term>Lymphedema</term>
<term>Purpura</term>
<term>Skin Diseases, Papulosquamous</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnostic" xml:lang="fr"><term>Dermatoses papulosquameuses</term>
<term>Lymphoedème</term>
<term>Purpura</term>
</keywords>
<keywords scheme="MESH" qualifier="malformations" xml:lang="fr"><term>Orteils</term>
</keywords>
<keywords scheme="MESH" qualifier="pathology" xml:lang="en"><term>Knee</term>
<term>Saphenous Vein</term>
<term>Thigh</term>
</keywords>
<keywords scheme="MESH" qualifier="surgery" xml:lang="en"><term>Saphenous Vein</term>
</keywords>
<keywords scheme="MESH" qualifier="therapy" xml:lang="en"><term>Lymphedema</term>
<term>Purpura</term>
<term>Skin Diseases, Papulosquamous</term>
</keywords>
<keywords scheme="MESH" qualifier="usage thérapeutique" xml:lang="fr"><term>Glucocorticoïdes</term>
</keywords>
<keywords scheme="MESH" xml:lang="en"><term>Child</term>
<term>Diagnosis, Differential</term>
<term>Female</term>
<term>Humans</term>
<term>Stockings, Compression</term>
<term>Syndrome</term>
<term>Treatment Outcome</term>
</keywords>
<keywords scheme="MESH" xml:lang="fr"><term>Bas de contention</term>
<term>Dermatoses papulosquameuses</term>
<term>Diagnostic différentiel</term>
<term>Enfant</term>
<term>Femelle</term>
<term>Humains</term>
<term>Lymphoedème</term>
<term>Purpura</term>
<term>Résultat thérapeutique</term>
<term>Syndactylie</term>
<term>Syndrome</term>
<term>Veine saphène</term>
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<front><div type="abstract" xml:lang="en">An 8-year-old girl referred to our Department for a two-month worsening of congenital primary lymphedema of the lower limb and for the appearance of several purpuric lesions on the right thigh and knee. We diagnosed a lichenoid pigmented purpura of Gougerot and Blum in a patient with Milroy disease, complicated by an insufficiency of anterior saphena. We treated the patient with topical steroids and compression stockings, until surgical intervention of phlebectomy. We report this case for the rarity of the disease, for the even more rare association with lichenoid pigmented purpura and for cutaneous immunopathological findings.</div>
</front>
</TEI>
<affiliations><list><country><li>Italie</li>
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<tree><noCountry><name sortKey="De Martino, Maurizio" sort="De Martino, Maurizio" uniqKey="De Martino M" first="Maurizio" last="De Martino">Maurizio De Martino</name>
<name sortKey="Duranti, Alberto" sort="Duranti, Alberto" uniqKey="Duranti A" first="Alberto" last="Duranti">Alberto Duranti</name>
<name sortKey="Lotti, Torello" sort="Lotti, Torello" uniqKey="Lotti T" first="Torello" last="Lotti">Torello Lotti</name>
<name sortKey="Moretti, Silvia" sort="Moretti, Silvia" uniqKey="Moretti S" first="Silvia" last="Moretti">Silvia Moretti</name>
<name sortKey="Panelos, John" sort="Panelos, John" uniqKey="Panelos J" first="John" last="Panelos">John Panelos</name>
<name sortKey="Pieri, Alessandro" sort="Pieri, Alessandro" uniqKey="Pieri A" first="Alessandro" last="Pieri">Alessandro Pieri</name>
</noCountry>
<country name="Italie"><noRegion><name sortKey="Berti, Samantha" sort="Berti, Samantha" uniqKey="Berti S" first="Samantha" last="Berti">Samantha Berti</name>
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Serveur d'exploration sur le lymphœdème

Purpura-associated congenital lymphedema.

Purpura-associated congenital lymphedema.

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri

Pour générer des pages wiki

	Serveur d'exploration sur le lymphœdème
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